Outcome of 14 Patients with Dandy Walker Malformation in Al Nasiriyah Teaching Hospital (2014 – 2020)

Abstract

       early workers. Although the Taggart and Walker theory has probably been the one most CSF path ways dilatation accompanied by a posterior compartment cavity& both cerebellar atrophy is known as Dandy Walker malformation, is a rare syndrome with facing a challenge in its presentation & management. The sign & symptom rely on congenital malformation in toddler. If the problem due to raised ICP the infant is presented with large size head& sign & symptom of CSF pathways dilatation. In older children, cerebellar atrophy principally imitate axial trunk instead of peripheral limb  ,intellectual retardation , papilledema & extra ocular muscle extirpation  are apparent . Materials:       By this retrospective  study 14 cases were collected , diagnosed and treated throw out our neurosurgical field in Nasiriyah teaching hospital from 2014 to 2020. The diagnosis depends on radiologic investigation. Presently, the most definitive diagnostic imaging method is magnetic resonance imaging. Outcome:      Surgical treatment of 10 cases with douple catheter of ventricular system & posterior cranial fossa sac.Four cases treated with standard shunt system originating in the lateral ventricle with aid of endoscope for fenestration of membrane responsible for non communication to facilitate creation of one compartment. Patient outcome good and discharged well. Conclusion:          DWS is a rare congenital brain abnormality, presenting usually in first year of life with enlargement of the head. In older children , it can be present with varied neurological symptom. It is diagnosed with advanced imaging & treated primarily with CP or VP shunting or both. Prognosis varies due to several factor , but an early diagnosis & appropriate treatment have a good prognostic value .